Airway Management in a Pediatric Patient with Xeroderma Pigmentosum: A Case Report

Seyedhejazi Mahin, Dehdilani Marjan, Gaffarlou Mehdi, Aliakbari Sharabiani Behzad

Abstract


Xeroderma pigmentosum (XP) is a rare genetic disorder with a recessive autosomal inheritance. It seems that total intravenous anesthesia (TIVA) is more appropriate than inhalational anesthesia as a method for maintenance of general anesthesia for xeroderma pigmentosum patients and the airway manipulation must be performed as little and noninvasive as possible. The aim of this report was to evaluate the specific considerations for airway management and anaesthesia in these patients.

Keywords: Xeroderma pigmentosum; Airway management; Pediatric; Anesthesia; Total intravenous anesthesia


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References


Soen M, Kagawa T, Uokawa R, Suzuki T. Anesthetic management of a patient with xeroderma pigmentosum. Masui. 2006; 55(2):215-7.

Hasanoglu A Gücüyener K, L Tümer et al. Association of xeroderma pigmentosum with thrombasthenia. Turk J Pediat, 1996; 38:261-264.

Masuda Y, Imaizumi H, Okanuma M, Narimatsu E, Asai Y, Namiki A. anesthesia for a patient with xeroderma pigmentosum. Masui. 2002; 51(2):169-71.

Miyazaki R, Nagata T, Kai T, Takahashi S. Anesthesia for a patient with xeroderma pigmentosum. Masui. 2007; 56(4):439-41.

Oliveira CR, Elias L, Barros AC, Conceição DB. Anesthesia in patient with xeroderma pigmentosum: case report. Rev Bras Anestesiol. 2003; 53(1):46-51.

Golzari SE, Mahmoodpoor A. Laryngeal mask airway in medical emergencies. N Engl J Med. 2014; 27;370(9):883. doi: 10.1056/NEJMc1315505#SA2.

Orosco RK, Wang T, Byrne PJ. Xeroderma pigmentosum in an African-American. ORL J Otorhinolaryngol Relat Spec. 2011;73(3):162-5.

Shrestha GS, Sah RP, Amatya AG, Shrestha N. Anaesthetic management of patients with Xeroderma pigmentosum. A series of three cases. Nepal Med Coll J. 2011; 13(3): 231-2.


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