Multi-nodular Desmoplastic Medulloblastoma in a Child: A Rare Radiological Physiognomy

Songping Zheng, Seidu A. Richard, Yiyun Fu, Yan Ju, Chao You

Abstract


Introduction: Nodular desmoplastic variant of medulloblastoma although very common, can present with very challenging radiological feature that mimics others lesions in the inferior and lower vermis in children. We present a case of rare radiological appearance of desmoplastic medullobastoma. Case Presentation: A one year and nine months old male presented with unstable walking and projectile vomiting of two weeks’ duration. He was apparently walking well prior this illness. The vomiting was usually in the morning and associated with headaches. Radiological imaging revealed very unusual masses in the cerebellum vermin region with obvious bilateral ventricular enlargement as well as the third ventricle, indicating hydrocephalus. Surgery was successful carried out and microscopic as well as immunohistochemistry confirmed desmoplastic medullobastoma. Conclusion: Desmoplastic medulloblastoma although not very rare can be very problematic in terms of radiological diagnosis. We are of the option that our imaging finding will throw more light on the radiological features of this tumor.

Keywords


Multi-nodular, Medulloblastoma, Desmoplastic, Hydrocephalus, Physiognomy

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DOI: http://dx.doi.org/10.7575/aiac.abcmed.v.7n.1p.49

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